Difficult Endotracheal Intubation in a Patient with Pseudoxanthoma Elasticum
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چکیده
منابع مشابه
Acute Angle Closure Glaucoma in a Patient with Pseudoxanthoma Elasticum
Dear Editor, Pseudoxanthoma elasticum (PXE), also known as Gröenblad-Strandberg syndrome, is an inherited multi-systemic disorder characterized by progressive mineralization and fragmentation of elastic fibers in various organs including the skin, eyes, and vascular system. The reported ocular manifestations of PXE include optic nerve drusen, angioid streaks, large regions of retinal pigment ep...
متن کاملPseudoxanthoma elasticum
Pseudoxanthoma elasticum (PXE) is a genetic metabolic disease with autosomal recessive inheritance caused by mutations in the ABCC6 gene. The lack of functional ABCC6 protein leads to ectopic mineralization that is most apparent in the elastic tissues of the skin, eyes and blood vessels. The clinical prevalence of PXE has been estimated at between 1 per 100,000 and 1 per 25,000, with slight fem...
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This case report involves tracheal intubation using i-gel® in combination with a lightwand in a patient with a difficult airway, classified as Cormack-Lehane grade 3. I-gel® was used during anesthesia induction to properly maintain ventilation. The authors have previously reported successful tracheal intubation on a patient with a difficult airway through the use of i-gel® and a fiberoptic bron...
متن کاملPseudoxanthoma Elasticum – Also a Lung Disease? The Respiratory Affection of Patients with Pseudoxanthoma Elasticum
BACKGROUND Pseudoxanthoma elasticum (PXE) is an autosomal-recessive mineralisation disorder caused by loss of function mutations in the ABCC6 Gen. Histological findings and data of an autopsy of a PXE-patient suggest a possible pulmonal calcification. So far, there exists no clinical data whether PXE patients actually are at high risk of developing pulmonary disorder. METHODS In a cross-secti...
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ژورنال
عنوان ژورنال: Anaesthesia and Intensive Care
سال: 1982
ISSN: 0310-057X,1448-0271
DOI: 10.1177/0310057x8201000114